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Ocular complications of SAVI: A unique case of bilateral uveitis and retinal vasculitis

Articolo
Data di Pubblicazione:
2024
Citazione:
Ocular complications of SAVI: A unique case of bilateral uveitis and retinal vasculitis / Menean, Matteo; Marchese, Alessandro; Modorati, Giulio; Favale, Rosa; Boscia, Francesco; Bandello, Francesco; Miserocchi, Elisabetta. - In: AMERICAN JOURNAL OF OPHTHALMOLOGY. CASE REPORTS. - ISSN 2451-9936. - 34:(2024). [10.1016/j.ajoc.2024.102046]
Abstract:
Purpose: To describe a case of bilateral panuveitis in a patient with Stimulator of Interferon Genes (STING)- Associated Vasculitis with Onset in Infancy (SAVI). Observations: A 45-year-old patient diagnosed with SAVI presented bilateral panuveitis and uncontrolled sec- ondary intraocular hypertension due to structural complications from uveitis. Multimodal imaging revealed the presence of intraretinal fluid and bilateral vasculitis. The patient was started with systemic methotrexate. Conclusions and importance: This case is essential to characterize ocular involvement in patients with SAVI. Awareness of these ocular manifestations is crucial for timely management and improvement of visual prognosis.
Tipologia CRIS:
1.1 Articolo in rivista
Elenco autori:
Menean, Matteo; Marchese, Alessandro; Modorati, Giulio; Favale, Rosa; Boscia, Francesco; Bandello, Francesco; Miserocchi, Elisabetta
Autori di Ateneo:
BANDELLO FRANCESCO
MISEROCCHI ELISABETTA
Link alla scheda completa:
https://iris.unisr.it/handle/20.500.11768/165376
Link al Full Text:
https://iris.unisr.it//retrieve/handle/20.500.11768/165376/225240/Savi%20syndrome%20.pdf
Pubblicato in:
AMERICAN JOURNAL OF OPHTHALMOLOGY. CASE REPORTS
Journal
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https://www.sciencedirect.com/science/article/pii/S2451993624000562?via=ihub
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